Superior mesenteric artery syndrome, gastroparesis and gerd. The purpose of this video is spread awareness about a rare, lifethreatening disease by sharing my story with the condition. Dec 03, 2017 the purpose of this video is spread awareness about a rare, lifethreatening disease by sharing my story with the condition. Superior mesenteric artery syndrome research awareness and support, bonham, texas. Superior mesenteric artery, sma, syndrome is a rare disorder. Introductionsuperior mesenteric artery syndrome is a rare condition. Laparoscopic duodenojejunostomy for treatment of superior mesenteric artery syndrome. Sma supplies the midgut up to the spleenic flexure. Five members of a family of eight, including the father and four daughters, presented with symptoms previously attributed to the superior mesenteric artery syndrome. Contrast upper gi study was performed that demonstrated an abrupt cutoff in the third portion of the duodenum with a massively distended.
Superior mesenteric artery syndrome smas was diagnosed in a 16yearold boy who presented with a short history of repeated vomiting associated with weight loss to the point of collapse. We report a case of a female patient presenting with abdominal pain and vomiting who developed superior mesenteric artery sma. It is relatively rare and can be hard to distinguish from other causes of intestinal obstruction. Superior mesenteric artery sma syndrome is an uncommon but well recognized clinical entity characterized by compression of the third, or transverse, portion of the duodenum between the aorta and the superior mesenteric artery. The syndrome may be imitated or caused by an eating disorder and having to distinguish the two from each other is very important since misdiagnosis can be really dangerous. This phenomenon may be caused by a number of factors, one of which being acute weight loss. Jun 01, 2015 superior mesenteric artery syndrome smas is caused by the compression of the superior mesenteric artery sma against the 3rd part of the duodenum creating a proximal intestinal obstruction. Some studies report the incidence of superior mesenteric artery syndrome to be 0. Superior mesenteric artery syndrome smas is a rare condition caused by compression of the third part of the duodenum between the superior mesenteric artery sma and the aorta, causing symptoms. After 1400 cm 3 of emesis was noted, a nasogastric tube was placed and 2500 cm 3 of gastric fluid was obtained overnight. Sanjadsakati syndrome and its association with superior. Apr 28, 2014 im going to answer in technical terms because i assume you asking the question means either you are a med. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 toll free.
Patients with sma syndrome, like those with gastroparesis and gerd, present with epigastric pain, bloating, nausea, vomiting and early satiety as well as heartburn and food regurgitation. Superior mesenteric artery syndrome coexists with nutcracker. The importance of mesenteric aneurysms and different procedures for treatment are discussed. Ct or ct angiogram is also superior to ultrasound because it can measure the reduced aortomesenteric angle and sh ow the gastric and duod enal dilatation at. The superior mesenteric artery syndrome is characterized by the compression of the third segment of the duodenum by the mesentery at superior mesenteric artery level and a resulting duodenal. Apr 17, 2015 superior mesenteric artery syndrome 1. Zimmermanc adepartment of radiology, long island college hospital, 339 hicks street, brooklyn, ny 11201, usa bdepartment of pediatric gastroenterology, long island college hospital, 339 hicks street, brooklyn, ny 11201, usa. This study aims at analyzing the clinical presentation, diagnosis, and management of sma syndrome. Aneurysms of the superior mesenteric artery and its. For language access assistance, contact the ncats public information officer. Click export csv or ris to download the entire page or use the checkboxes to select a subset of records to download export. Superior mesenteric artery syndrome symptoms, causes, diagnosis, and treatment information for superior mesenteric artery syndrome superior mesenteric artery syndrome with alternative diagnoses, fulltext book chapters, misdiagnosis, research treatments, prevention, and prognosis. Superior mesenteric artery sma syndrome is a form of. The ctscan was performed to screen the cause of abdominal pain.
Superior mesenteric artery sma syndrome also known as wilkies syndrome is a rare condition caused by the entrapment of the third part of the duodenum between the aorta and the sma. In five cases in group a, all of the investigated clinical findings i. Superior mesenteric artery syndrome smas is caused by the compression of the superior mesenteric artery sma against the 3rd part of the duodenum creating a proximal intestinal obstruction. Superior mesenteric artery sma syndrome, also known as wilkies syndrome and cast syndrome, is a rare gastrointestinal disease that leads to obstruction of the duodenum. The patient will present with bloating after meals, nausea and vomiting and a feeling of abdominal fullness. Superior mesenteric artery syndrome is suggested the 3 rd part of the duodenum is compressed between the aorta and the superior mesenteric artery with consequential dilatation of the proximal duodenum and stomach. Diagnostic techniques done for smas can be very hard and tricky. Ct scan of the abdomen shows hugely distended stomach, first and second part of the duodenum, with transition zone at the origin of the sma, confirming the diagnosis of sma syndrome. Superior mesenteric artery syndrome associated with rapid. Introduction superior mesenteric artery syndrome smas mostly occurs i n adolescent or young adults and is a rare disorder. Superior mesenteric artery syndrome evidence search nice. Symptoms vary based on severity, but can be severely debilitating. Diagnosis superior mesenteric artery syndrome an abdominal computed tomography ct scan with contrast revealed the narrowing of the third portion of the duodenum compressed by the superior mesenteric artery sma, with dilation of the portion of the duodenum proximal to the compression.
Superior mesenteric artery syndrome is a rare cause of proximal small. Laparoscopic management of superior mesenteric artery syndrome. See how superior mesenteric artery syndrome is diagnosed. Superior mesenteric artery syndrome, new advances in the basic and clinical gastroenterology, thomas brzozowski. The full text of this article is available in pdf format. Superior mesenteric artery syndrome or wilkie syndrome is an acquired rare vascular compression disorder due to acute angling of the superior mesenteric artery sma resulting in compression of the 3rd part of the duodenum leading to obstruction. Superior mesenteric artery syndrome this is a rare disease that occurs when the duodenum is trapped between the abdominal aorta and the superior mesenteric artery, causing compression or complete obstruction. Studies to determine the optimal methods of diagnosis and treatment are required. Volume 11 issue 2 computed tomography and ultrasonography in superior mesenteric artery syndrome 93 consisted of 10 females and 3 males, whereas group b consisted of 34 females and 42 males. Obstruction of the third part of the duodenum d3 is a very rare cause of gastric outflow obstruction.
Pals patient airlift services patient airlift services pals arranges free air transportation for individuals requiring medical diagnosis, treatment or followup, for compassionate assistance, f. This syndrome is variably called as arterial mesenteric duodenal compression, cast syndrome or wilkies syndrome. The superior mesenteric artery sma syndrome is a rare entity presenting with upper gastrointestinal tract obstruction and weight loss. The differential diagnosis includes anorexia nervosa and bulimia. In addition, superior mesenteric artery sma syndrome should be differentiated from other causes of megaduodenum or duodenal ileus, including diabetes mellitus, collagen vascular conditions, and chronic idiopathic intestinal pseudoobstruction.
Minimally invasive surgery for superior mesenteric artery syndrome. Health, general arterial occlusions care and treatment case studies diagnosis arterial occlusive diseases gastrointestinal diseases. Case report superior mesenteric artery syndrome and its. It has been referred to by a variety of other names, including cast syndrome, wilkie syndrome, arteriomesenteric duodenal obstruction, and chronic duodenal ileus. Patients seen in acute rehabilitation settings, not uncommonly, have a period of rapid weight loss. Aug 06, 2015 superior mesenteric artery syndrome or wilkie syndrome is an acquired rare vascular compression disorder due to acute angling of the superior mesenteric artery sma resulting in compression of the 3rd part of the duodenum leading to obstruction. Superior mesenteric artery sma syndrome is a rare disorder, characterized by compression of the third segment of. Definition of mesenteric ischemia infarction and necrosis through the mesenteric ischemia.
Superior mesenteric artery syndrome genetic and rare diseases. This exploration revealed small bowel ischemia with a parietal thickening and, at the early arterial phase, a 90% reduction of the superior mesenteric artery sma lumen 2 cm from its origin fig 1, combined with a slight ectasic aspect of the origin of the celiac artery. Its is a difficult syndrome to diagnose as alot of drs. Mesenteric artery disease healthcare baylor college of. The syndrome is characterized by compression of the third portion of the duodenum due to.
Its also to explain what happened during this time because most people. The superior mesenteric artery sma syndrome is an atypical cause of high intestinal obstruction in adults. The laboratory results on presentation revealed a bun 25 and a creatinine 1. Superior mesenteric artery syndrome, gastroparesis and. Superior mesenteric artery syndrome rani sophia and waseem ahmad bashir yeovil hospital nhs foundation trust, yeovil, somerset united kingdom 1. Mesenteric or intestinal artery disease is a condition that develops when the arteries in the abdomen that supply the intestines become narrowed, or blocked, by an accumulation of a fatty substance called plaque. Closure of the inferior mesenteric artery usually has a mild course. Superior mesenteric artery sma syndrome is a gastrovascular disorder in which the third and final portion of the duodenum is compressed between the abdominal aorta aa and the overlying superior mesenteric artery. Superior mesenteric artery sma syndrome arises from a reduction in the angle formed between the sma and the aorta, thereby compressing the third portion of the duodenum.
If you have problems viewing pdf files, download the latest version of adobe reader. This results in chronic, intermittent, or acute complete or partial duodenal obstruction. We are a registered nonprofit with the ultimate goals of raising awareness of. Superior mesenteric artery syndrome and nutcracker phenomenon. Superior mesenteric artery syndrome my story youtube. Is there a cure for the superior mesenteric artery syndrome. Statistics of superior mesenteric artery syndrome 23 people with superior mesenteric artery syndrome have taken the sf36 survey. To access free multiple choice questions on this topic, click here. Superior mesenteric artery sma syndrome clinical presentation.
However, after extensive research, original data establishing this mortality rate has not been found, indicating that the number is likely to be unreliable. We describe three patients with aneurysms in the sma or its branches found at angiography in our department. Superior mesenteric artery syndrome a rare presentation. It is a rare but lifethreatening syndrome caused by inadequate flow of blood through the mesenteric vessels resulting in ischemia and gangrene of the bowel wall. Familial superior mesenteric artery syndrome springerlink. Superior mesenteric artery syndrome stacismasnpo on. Superior mesenteric artery syndrome a rare presentation and. Im going to answer in technical terms because i assume you asking the question means either you are a med. After resuscitation and investigation, he was treated surgically. Superior mesenteric artery syndrome and its ramifications. This familial clustering raises the possibility of a genetic predisposition to this symptom and radiographic complex. Clinical report by journal of evolution of medical and dental sciences. Superior mesenteric artery syndrome causes, symptoms, diagnosis, treatment. Superior mesenteric artery sma syndrome differential diagnoses.
A 1in3 mortality rate for superior mesenteric artery syndrome has been quoted by a small number of sources. An indication of a mesenteric infarction is given by blood on the finger stall during the. Superior mesenteric artery syndrome symptoms, treatment. Aneurysms of the superior mesenteric artery sma and its branches are rare. A collection of disease information resources and questions answered by our genetic and rare diseases information specialists for superior mesenteric artery. Case report superior mesenteric artery syndrome and its rami.
Radiological modalities play a major role in its diagnosis and surgical methods remain the gold standard in its management. History, physical, causes superior mesenteric artery sma syndrome is an uncommon but well recognized clinical entity characterized by compression of the third, or transverse, portion of the duodenum between the aorta and the superior mesenteric artery. Downloaded free from on thursday, march 03, 2016, ip. Read more about symptoms, diagnosis, treatment, complications, causes and prognosis. Please share the word and ask your friends to shop through our link.
Amazon prime days is coming up and its a great time to help the nonprofit raise a little money. This compression causes partial or complete blockage of the duodenum. Superior mesenteric artery syndrome 417 lee, mangla 1978. Apr 27, 2017 superior mesenteric artery syndrome, gastroparesis and gerd. Superior mesenteric artery syndrome smas is a digestive condition that occurs when the duodenum the first part of the small intestine is compressed between two arteries the aorta and the superior mesenteric artery. Aneurysms of the superior mesenteric artery and its branches. Which specialists are essential to meet, what tests are needed and other useful information for the diagnosis of superior mesenteric artery syndrome. Superior mesenteric artery sma syndrome differential. Superior mesenteric artery sma syndrome is a gastrovascular disorder in which the third and. The four daughters also had radiographic studies supporting that diagnosis.
How is superior mesenteric artery syndrome diagnosed. Superior mesenteric artery syndrome is an unusual cause of proximal intestinal obstruction. Superior mesenteric artery syndrome statpearls ncbi bookshelf. Superior mesenteric artery sma syndrome is an unusual cause of vomiting and weight loss resulting from the compression of the third part of the duodenum by the sma. Results for superior mesenteric artery syndrome 21 30 of 74 sorted by relevance date. Superior mesenteric artery syndrome genetic and rare. Superior mesenteric artery syndrome is a rare condition, causing intestinal obstruction. Superior mesenteric artery syndrome smas mostly occurs i n adolescent or young adults and is a rare disorder. Read more about symptoms, diagnosis, treatment, complications, causes.
The superior mesenteric artery syndrome smas is characterized by the compression of the third segment of duodenum by the mesentery at sma level, and a resulting duodenal gastric dilatation 16. The condition occurs when the duodenum the part of the small. Case discussion superior mesenteric artery syndrome. Mesenteric ischemia bowel infarction therapy and ortners. Mesenteric ischemia bowel infarction diagnosis, therapy, and ortners syndrome. Acute pancreatitis and superior mesenteric artery syndrome. Superior mesenteric artery syndrome radiology case.
Superior mesenteric artery sma syndrome is a rare condition that involves the small intestine. Occurs when duodenum is compressed between aorta and superior mesenteric artery. Mean of superior mesenteric artery syndrome is 0 points 36 %. Jul 05, 2015 inferior mesenteric artery the inferior mesenteric artery is the artery of hindgut it arises from the anterior or left anterolateral aspect of the aorta at about the level of third lumbar vertebra 3 or 4 cm above the aortic bifurcation. Jun 14, 2018 superior mesenteric artery syndrome smas is a digestive condition that occurs when the duodenum the first part of the small intestine is compressed between two arteries the aorta and the superior mesenteric artery. Total score ranges from 0 to 3,600 being 0 the worst and 3,600 the best. The patient was afebrile and vital signs were stable.